This document summarizes the management of single ventricle physiology from birth through surgery. It identifies how infants with this condition present, including shock, cyanosis, or heart failure. Key aspects of pre-operative stabilization include identifying obstructions to pulmonary or systemic blood flow and whether the atrial septum is restrictive. Surgical options like the Norwood procedure are described which aim to balance circulations prior to a Fontan-type completion. Post-operative care focuses on monitoring oxygen delivery and adjusting pulmonary and systemic resistances through ventilation or drugs.

1. Single Ventricle Physiology Spectrum of Management from Birth to Surgery Dr. J. Burzynski Division of Pediatric Critical Care University of Iowa

10. Hypoplastic left heart syndrome (HLHS) 1 - patent foramen ovale 2 - pinched aorta 3 - patent ductus arteriosus 4 - narrowed aorta 5 - hypoplastic left ventricle 6 - aortic atresia Complete mixing at atrial level through PFO

11. Interrupted aortic arch 1 - interruption of aortic arch 2 - descending aorta connected to pulmonary artery by large patent ductus arteriosus 3 - ventricular septal defect

27. NORWOOD OPERATION

28. DKS AND ARCH REPAIR

30. Sano shunt with augmented aortic arch Beginning of arch augmentation

37. The END! …