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Total anomalous systemic
venous drainage to the left
atrium
A Sharp eye on left atrial isomerism is must
Introduction
Classification TASVD
Type I Type II Type III
IVC to left-sided atrium IVC interruption IVC to accessory chamber (like
coronary sinus)
 Type A: Hepatic veins to left-
sided atrium
 Type B: Hepatic veins to
other site
Zhang ZW, Duan QJ, Gao Z, Ru W, Ying LY. Total anomalous
systemic venous drainage to the left atrium. Ann Thorac Surg
2009;87:1599-601-13
Embryology
• Failure of regression of the right valve of systemic venous sinus (sinus
venosus)
• Systemic venous sinus being incorporated into the left atrium
Hemodynamic
• Left atrium forms the mixing chamber in the circuit
• Similar to the case of a total anomalous pulmonary venous drainage
• Oxygen saturation is equal in all the chambers
Diagnosis
• Echocardiography with agitated saline contrast follow up(caution :air
embolism to brain and coronary)
• CT scan helps confirm drainage of all veins
Treatment
• Surgery
Think before you choose

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Total anomalous systemic venous drainage