Dr. Chris Halpin discusses findings in audiology with respect to Norrie Disease. He concludes with a discussion of hearing aids for people with Norrie Disease. (NDA International Conference, 2009)
Audiology in Norrie Disease: Research and Hearing Aids
1. Chris Halpin, Ph.D.
Massachusetts
Eye and Ear
Infirmary
Harvard
Medical
School
August 14, 2009
First International
Norrie Disease Association Conference 2009:
AUDIOLOGY IN NORRIE DISEASE:
RESEARCH
AND HEARING AIDS
15. 2000 Hz THRESHOLDS BY AGE
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U.S. Costa Rica
WORD RECOGNITION BY AGE
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axes.2.asy.outly.sp
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Thanks.19
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Import.yr
29. In 2008, about 1.4 Million People
Bought 2.4 Million Hearing Aids
They Are Now $1500 - $3500 each; 5B
About 31 Million Americans “Have Hearing Loss”
And 7 Million Have Bought Hearing Aids
About Half Are “Satisfied”
Many Do Not Wear
Hearing Aids Have a Bad Reputation
Which Is Addressed With Anecdotes of Success,
Promises of New Technology
HEARING AIDS
30. In 2007, about 1.4 Million People
Bought 2.4 Million Hearing Aids
They Are Now $1500 - $3500 each; 5B
About 31 Million Americans “Have Hearing Loss”
And 7 Million Have Bought Hearing Aids
About Half Are “Satisfied”
Many Do Not Wear
Hearing Aids Have a Bad Reputation
Which Is Addressed With Anecdotes of Success,
Promises of New Technology
HEARING AIDS
52. “So, Can you make it too loud with no whistle?”
advice
53. “So, Can you make it too loud with no whistle?”
Mine doesn’t have a volume control...
54. “So, Can you make it too loud with no whistle?”
“It’s Whistling...
That’s how I know it’s too loud.”
(WRONG)
That’s how we know
It’s too limited.
55. “So, Can you make it too loud with no whistle?”
“It’s Whistling...
That’s how I know it’s too loud.”
(WRONG)
That’s how we know
It’s too limited.
56. “So, Can you make it too loud with no whistle?”
People’s voices are too loud (Jackpot!)
57. “So, Can you make it too loud with no whistle?”
“I don’t like it, but it’s easier to hear people”
“I turn it down a little so it doesn’t drive me crazy”
(OK)
Hearing aids should be loud…
to reduce the workload of communicating.
People’s voices are too loud (Jackpot!)
59. National Temporal Bone Donor Program
• Enlists people with otologic
disorders to become
temporal bone donors
• Registry arranges the
pledge, obtains medical
records, and updates
records periodically
64. Anecdotes:
“I tried the new Zipzip 440
and they loved it”
“This thing is no good. You
ripped me off...”
“I baked you these
cookies...”
dif is coch calc
65. “So, Can you make it too loud with no whistle?”
Is It On? I guess so...
Is It Too Loud? No...
unclear
67. Distortion Product Otoacoustic Emissions:
Age 14
-20
-10
0
10
20
1000 2000 3000 4000 5000 6000
Geometric Mean of F1 and F2
dBSPL
Noise L
DP L
Noise R
DP R