SlideShare una empresa de Scribd logo
1 de 81
Aortic Arch Anomalies
 Hunault in 1735,cited by Moes -wrote pathologic description of
anomalous right subclavian artery.
 Double aortic arch-Hunault 1735
 First report of clinical syndrome of vascular compression-wolman
1939
 Kommerel in 1936 –xray findings of anamolous right sca
 first division of a vascular ring -Gross in 1945
 first successful repair of interrupted aortic arch-Merrill et al. in 1957 .
classifications
• Stewert etal and shuford ,syber etal
– Side of aortic arch
– Origin of brachiocephalic vessels
– Site of DA/LA
• Freedom etal-vascular ring/sling/compression
• sissman-Ao.arch position,course,length,size
Anatomical Classification
 following anatomic categories:
1)Abnormalities of branching,
2)Abnormalities of arch position including right aortic arch &
cervical aortic arch,
3)Supernumerary arches including double aortic arch and
persistent fifth aortic arch,
4)Interrupted aortic arch
5)Anomalous origin of a pulmonary artery branch from the
ascending aorta or from the contralateral pulmonary artery branch.
Embryology
 The specific anomalies better understood through appreciation of
their embryologic origins.
 Development of the aortic arch system - best be described as-
sequential appearance and persistence or regression of 6 paired
vessels connecting the truncoaortic sac of the embryonic heart tube
with the paired dorsal aortae, which fuse to form the definitive
descending aorta.
• Fate of the aortic arches:

First pair: A small part forms the maxillary
artery, the rest disappears.
 Second pair: A small part forms the
stapedial & hyoid arteries, the rest
disappears.
 Third pair: forms the common, internal &
external carotid arteries on each side.
 Fourth pair: forms the aortic arch (AA) on
the left side, and the right subclavian (RSC)
artery on the right side.
 Fifth pair: totally disappears.
 Sixth pair: forms the right & left pulmonary
arteries (PA) and the ductus arteriosus (DA).
Left and Right Arch Definition
 Left and right aortic arch- refer to which bronchus is crossed by the
arch, not to which side of the midline the aortic root ascends.
 Sidedness determined with Echo or angiography by the branching
pattern of the brachiocephalic vessels.
 General rule – 1st arch vessel contain a carotid artery. contralateral to
Aortic Arch
The 3 brachiocephalic br. of the arch are derived from:
- The innominate artery -Rt br. of the truncoaortic sac
- Rt common carotid artery-Rt 3rd embryonic arch
- Rt subclavian -Rt 4th arch and (proximal) Rt dorsal
aorta proximally and Rt 7th ISA distally;
- Lt carotid artery -Lt 3rd aortic arch;
- Lt subclavian artery from Lt 7th ISA.
Diagnostic Methods
 1930s, barium esophagography - primary method for diagnosing
arch anomalies.
 In the 1960s and 1970s, angiography became the gold standard .
 In the last 10 to 15 years, MRI and CT, have supplanted angiography
as the gold standard for definitive diagnosis of arch anomalies.
 Both modalities have the advantages of large fields of view and
simultaneous visualization of vessels and airways, and both are
minimally invasive.
Edwards hypothetical double arch
concept
Clinical Classification
 In addition to the anatomic categorization , arch anomalies divided
according to clinical features as follows:
-Vascular rings;
-Non ring vascular compression of the trachea, bronchi, or
esophagus;
- Noncompressive arch malformations;
-Ductal-dependent arch anomalies including interrupted aortic
arches
- Isolated subclavian, carotid, or innominate arteries.
- Genetic syndromes and associated abnormalities.
Vascular Rings
 In this anomaly trachea and esophagus are completely surrounded by
vascular structures.
 The vascular structures need not be patent, e.g., a ligamentum
arteriosum or atretic segment of aortic arch may complete a ring.
 clinical presentation - stridor, pneumonia, bronchitis, or cough .
 Infants may - posture of hyperextension of the neck.
 Less commonly, pts exhibit reflex apnea associated with eating..
 Less commonly in toddlers or older children- swallowing difficulty or
choking .
 When all elements of the ring are patent, visualization, especially by
tomographic imaging, is straightforward.
 In cases where the ring is completed by an atretic segment of aorta or
ligamentum arteriosum, those segments cannot be visualized with
current imaging technologies.
 But these rings are recognizable by the presence of one of three
opposite the side of the aortic arch: diverticulum, dimple, or
descending aorta .
Normal Left Aortic Arch and variants
 normal left aortic arch crosses the left mainstem bronchus at T5 and
descends left of the midline to the diaphragm and beyond in cases of
visceral situs solitus.
 normal branching pattern has the right innominate artery first.
 branches into the Rt CCA and Rt subclavian arteries
 Lt carotid artery second, and the Lt subclavian artery third.
 Ductus arteriosus or the ligamentum arteriosum joins the aorta distal
to Lt subclavian artery .
 2 frequent variants of the Lt aortic arch.
 -1)Common brachiocephalic trunk, in which the right innominate
and left carotid arteries arise from a single origin.
Present in10% of otherwise normal left arches
No consequence,
Some have suggested that innominate artery compression of the
trachea is more frequent when common brachiocephalic trunk is
present.
-
2)Separate origin of the Lt vertebral artery from the aortic arch
proximal to the takeoff of the lt SCA rather than from the SCA .
• Seen in 10% of normal left arches ,No functional significance
•
• should not be confused with anomalous Rt SCA in which there
are also four brachiocephalic vessels .
• Distinguishing feature
3-D MRI of normal variant with separate
origin of left vertebral artery (L Vert) from
the aortic arch
Left Aortic Arch with Retroesophageal Rt SCA
 first described by Hunauld in 1735.
 Also called anomalous or aberrant right subclavian artery
 Bayford coined the term dysphagia lusoria•(from the Latin, lusus
naturae, trick of nature).
 The branching pattern
1st branch - Rt CCA
2nd - Lt CCA
3rd - Lt SCA
4th - retroesophageal Rt SCA arising from the
posteromedial aspect of the distal aortic arch
 Most common arch anomaly,
 Seen in 0.5% of the general population.
 The incidence in Down syndrome patients with congenital heart
disease is very high at 38% .
 Mostly asymptomatic, with the diagnosis made while imaging for
another condition or at autopsy.
assoc
• TOF and left aortic arch-
• COA-
– may arise distal to coarct site. If so:
– BP in RUL and LL does not reflect coarct. Gradient
– Rib notching seen only on left side
 Diagnosis and Management
 Since there is no innominate artery, 1st & 2nd branches, (Rt&Lt CA)
similar in size as are the last 2 branches( Lt &Rt SCA)
 Barium esophagography
- Fixed filling defect usually slanting upward to the right
 Angiography
-The diagnosis may sometimes be missed in the AP projection since
the right subclavian may be superimposed on the right carotid artery
in the usual position.
-
Careful single-frame analysis will demonstrate the earlier filling of the
right carotid on an aortic root injection or the earlier filling of the right
subclavian on a descending aortic injection.
Barium esophagogram
Echocardiography -
-Branching pattern , a nonbifurcating first branch that ascends
toward the right, followed by two successive left-sided vessels
(left carotid and left subclavian arteries) followed by a fourth
branch that heads toward the right but may disappear behind
the trachea.
 MRI
- The retroesophageal course of the subclavian artery is shown
on transverse (axial) cuts.
• If symptomatic-
– Division of anamolous RSCA
– Dissection of retroesophageal component if any
– Reanastomosis of vessel
• Establishing flow in RSCA- important.
• Approach in pt with vascular ring-
– right thoracotomy
Left Aortic Arch with Retroesophageal
Diverticulum of Kommerell
 Very rare arch anomaly
 1st vascular ring to be diagnosed in life with
barium esophagography by Kommerell
 branching pattern identical to that of the
more common left arch with
retroesophageal right subclavian artery
 The difference is in the caliber of the
proximal subclavian artery .
 significance - is that the abrupt change of
vessel size always indicates the presence of
a ligamentum arteriosum, which completes
a vascular ring.
Left Aortic Arch with Right Descending
Aorta and Right Ductus (or Ligamentum)
 Rare arch anomaly, also known as circumflex aortic arch, with a
branching pattern similar to that of left arch with retroesophageal right
subclavian artery.
 The arch itself is retroesophageal; hence the right subclavian artery,
although it may arise as the last arch vessel, is not retro-esophageal .
 The descending aorta is connected by a ductus or ligamentum to the
right pulmonary artery, forming a vascular ring.
Left Aortic Arch with Isolated SCA
 Rare anomaly, subclavian artery arises only from the ductus
arteriosus.
 If ductus is patent, the subclavian and vertebral arteries are supplied
from the pulmonary artery.
 When the ductus closes, the subclavian is supplied by retrograde flow
from the vertebral artery via the circle of Willis.
 Embryology
 This occurs with dissolution of the right fourth arch and right dorsal
aorta but persistence of the right sixth arch.
 Diagnosis and Management
 in the absence of other anomalies, it may go unrecognized or may
cause vertebrobasilar insufficiency with so-called congenital
subclavian steal.
 With phase-encoded velocity mapping, retrograde flow in the
vertebral artery can be detected on MRI.
 Symptomatic patients are treated by implantation of the subclavian
artery into the aorta.
Left Aortic Arch with Cervical Origin of
the Right Subclavian Artery
 Found in pts with TOF, with or
without pulmonary atresia,
 Seen only in patients with 22q11
deletion .
 marker for CATCH 22.
 Normally the right innominate artery
bifurcates into a Rt CCA and Rt
SCA near its origin from the aorta .
 In this Innominate trifurcates in the
neck, giving rise to external and
internal carotids and the SCA, which
then travels caudally back to the
thorax.
 Embryology
Rt subclavian artery originates from the third arch, which is more
cephalad than the fourth, gives origin to the subclavian artery in the
neck rather than in the thorax.
Right Aortic Arch
 A single aortic arch that crosses over the right main stem bronchus,
passing to the right of the trachea.
 There are four major types of right arch:
(a) with mirror image branching,
(b) with retroesophageal left subclavian artery,
(c) with retro-esophageal diverticulum, and
(d) with left descending aorta.
There are also several infrequently occurring variations.
 Incidence
- InTOF 13% to 34% . Of these-93% mirror image br
-TA -36%-( generally higher than in TOF)
DORV-20% -TGA 3%(assoc with VSD and PS 16%)
Right Aortic Arch with Mirror-Image Branching
 1st branch is Lt innominate artery, divides into Lt carotid and Lt
SCA
 2nd Rt carotid, 3rd a Rt subclavian .
 left-right mirror of a normal left aortic arch.
 But ..
 ductus arteriosus (or ligamentum arteriosum) is usually the left-sided
one, arising from the base of the innominate artery rather than from
the aortic arch.
 Therefore ligamentum does not form a vascular ring.
 Almost always associated with congenital intracardiac disease.
 Diagnosis and Management
 usually produces no retro-esophageal compression or vascular ring,
 no symptoms produced by the arch itself.
 Diagnosis - usually made during imaging of the assoc congenital
intracardiac disease.
 Diagnosed by distinctive branching pattern in echo and angiography,
and appearance of a right-sided indentation of trachea and esophagus
on plain radiograph and barium esophagography.
 No treatment of right aortic arch is required
 It may be helpful for surgeons to know the sidedness of the aortic arch
in certain circumstances.
 For the classical B –T shunt and modified form are best carried out
using the side with an innominate artery.
Right Aortic Arch with Retroesophageal
Diverticulum of Kommerell
 Second most common vascular ring after double aortic arch.
 Branching
1st branch -Lt CCA
2nd Rt CCA
3rd Rt SCA
4th - a retro-esophageal vessel from which the Lt SCA arises and the
left ductus arteriosus or ligamentum arteriosum connects.
 This combination of vessels produces a vascular ring.
 Diagnosis and Management
 The presenting symptoms are usually that of a vascular ring.
 Appearance of a right aortic arch on a plain CXR .
.
 . Echo -Lt carotid artery arising alone as the first arch vessel,
-Diverticulum followed to the point at which the caliber
changes to that of the smaller subclavian artery.
 Angiography- characteristic branching pattern
- abrupt change in caliber from diverticulum to
subclavian artery.
 MRI - ideal for making this diagnosis
- noninvasive and have the ability to display both vascular and
airway structures.
 Most people are asymptomatic.
 Treatment is surgical division of the ductus or ligamentum in those
patients who are symptomatic.
 In those patients undergoing surgery for another lesion, even an
asymptomatic ligamentum should be divided.
Right Aortic Arch with Retroesophageal
Left Subclavian Artery
 Arch passing to the right of the trachea
 Sequence of brachiocephalic arteries:
- Left carotid,
- Right carotid,
- Right subclavian,
- and retroesophageal left subclavian .
 This differs from the previous arch in that the proximal left subclavian
artery is not significantly larger in caliber than its more distal portion
(i.e., no aortic diverticulum).
 Therefore, there is no left-sided ductus arteriosus or ligamentum
arteriosum and thus no vascular ring.
 Many of these patients have associated conotruncal anomalies.
 Diagnosis and Management
 suspected from barium EsoG -a relatively small posterior indentation
on the esophagus passing upward to the left.
 No vascular ring, the trachea is unaffected except for the slight
leftward deviation .
 Echo- identify the first branch of the aorta as a left carotid artery
 Both MRI and angiography can demonstrate the size of the left
subclavian artery, which distinguishes this lesion from right aortic
arch with retroesophageal diverticulum.
 Since there is no vascular ring, there is usually no need for treatment
other than that of associated anomalies.
Right Aortic Arch with Left Descending
Aorta and Left Ductus Arteriosus or
Ligamentum Arteriosum
 Also known as right aortic arch with retroesophageal segment or
circumflex right aortic arch
 Presentation similar to right arch with retro-esophageal diverticulum
 It is the aortic arch that is retroesophageal, not the subclavian artery or
an aortic diverticulum.
Diagnosis and Management
The findings on CXR and barium esophagography
may be similar to those in right arch with
retroesophageal diverticulum.
 Differences include a downward to the left instead
of upward to the left orientation of the esophageal
indentation .
 Order of brachiocephalic artery branching.
 In the case of right aortic arch with left descending aorta, the first
vessel contains the left carotid artery.
 MRI can avoid some of the pitfalls seen with projection images and
can delineate the entire aorta, its relationship to the trachea .
 Division of the vascular ring when patients are symptomatic.
Right Aortic Arch with Retroesophageal
Innominate Artery
 Rare abnormality of the aortic arch system.
 Contrary to the general rule that the first arch vessel contains a
carotid artery contralateral to the aortic arch, in these cases the
sequence of brachiocephalic vessels is right carotid, right subclavian,
retroesophageal left innominate artery .
 The ductus arteriosus or ligamentum arteriosum completes a vascular
ring as it connects the left pulmonary artery with the base of the so-
called innominate artery.
 Diagnosis and Management
 Tracheal compression seems to be the rule.
 The important anatomic clues to the diagnosis by any imaging
modality are the presence of a single carotid artery arising from the
proximal aorta.
 The other anomalies with that finding are also rare: Interrupted aortic
arch with interruption between the two carotid arteries and isolated
left carotid or innominate artery.
Cervical Aortic Arch
 Rare anomaly ,
 Apex above the clavicle (as high as the C2 ).
 Seperate origin of carotid artery contralateral to arch with seperate
origin if ICA,ECA,SCA on arch side
 2 main subcategories
- Those with anomalous subclavian artery and vascular ring, with
either descending aorta c/l to the arch or retroesophageal diverticulum
-And those with a virtual normal branching pattern.
 The first and larger group usually has a right aortic arch. .
 Separate origin of the vertebral artery from the arch can be seen in
each of the groups.
 The second group typically has a left aortic arch. .
 Stenosis or atresia of the origin of the left subclavian artery is
sometimes seen in either group .
 Diagnosis and Management
 Presents as pulsatile masses in the supraclavicular fossa or in the neck.
 In infants, prior to the appearance of mass, presenting signs may be
those of a vascular ring like , stridor, dyspnea, or repeated LRTI.
 In adult, the most likely symptom from a vascular ring is dysphagia.
 In patients with stenosis or atresia of the left subclavian artery and
origin of the ipsilateral vertebral artery distal to the obstruction, a
subclavian steal may exist with CNS symptomatology.
 In the presence of a pulsatile neck mass, brief compression of the
mass results in loss of femoral pulses .
 CXR -cervical arch may be suspected by the presence of a widened
upper mediastinum and the absence of the aortic knob.
 Evidence of anterior deviation of the trachea is in favor of the
diagnosis.
 Treatment is necessary if the cervical arch is complicated by arch
hypoplasia, symptomatic vascular ring, or rarely, aneurysm of the
cervical arch itself .
 Persistance of both emb.aortic arches with separate origin of CA and
SCA
 therefore-NO innominate artery
 DA-almost always left sided
 A ductus arteriosus or ligamentum may be present-not an essential
element but length may affect-degree of compression
 both arches-usually patent although one is larger
Double Aortic Arch
When desc. Aorta is to left of spine- Right arch –larger
–more posterior-75% cases(MC)
The right arch is the more superiorly located.
When desc.aorta is right of spine-left arch –more
posterior-larger-75-85% cases
Rule-desc aorta is contralateral to side of dominant arch
All double aortic arches technically form complete
vascular rings around the trachea and esophagus.
Usually occurs without assoc. CHD.but assoc-22%
cases-TOF ,TGA
• Although hypoplasia is common segmental
atresia uncommon usually left.
• Shuford and sybers classification
 Embryology
 Persistance of both paired dorsal aortic arches –failure of regression of
right 8th somatic segment of right dorsal aorta
 Right DA regresses in majority
 One of the arch may be atretic- may occur at any segment
 Complete vascular ring
 Peristance of DA on either side not needed to complete vasc.ring like
other forms .
 Double arch with atretic left arch is more commonly associated with
22q11 deletions syndromes than double arch with both widely patent.
 Diagnosis and Management
 MC clinically recognised form of vascular ring
 Severely sympto.-infancy-stridor,dyspnea,cough,recurRTI.
 Feed poorly,
 Prefer opisthotonus
 Life threatening episodes of reflex apnea with cyanosis may.
 Routine chest xray often suggests.
 Hyperinflation of either/both lungs
 Barium esophagography-b/l indentations of eso in AP proj
 Large oblique defect(retroeso arch)
 But often not possible to diff from right arch with ana.Left SCA
 Angiography of asc aorta.
The diagnosis of double arch with both arches patent
can sometimes be made convincingly from the plain
CXR.
The tracheal air column is indented by the more
superior, right-sided arch and the more inferior left arch.
In the lateral view, the right arch can be seen to indent
the trachea posteriorly.
 Confirmation by echo, angiography, or MRI is important to identify
the hypoplastic segment to divide it.
.
 Echo-Suprasternal views-coronal plane-b/l echolucencies of double
arch
.
 MRI-side of dominant arch and patency of minor arch- spatial
relationships of vessels, trachea, and esophagus for surgical planning
.
 Surgical division of the vascular ring in any patient who is
symptomatic with airway or esophageal compression or in a patient
undergoing surgery for intracardiac disease.
Persistent Fifth Aortic Arch
 First reported in man by Van Praagh in 1969 as a double-lumen
aortic arch in which both arches appear on the same side of the
trachea.
 In double aortic arch each arch is on the opposite side.
 Subcategorization :
- Double-lumen aortic arch with both lumina patent
-Atresia or interruption of the superior arch with patent inferior
(persistent fifth) arch common origin of all brachiocephalic vessels
from the ascending aorta .
 Diagnosis and Management
 Recognized either by angiography or at postmortem examination, with
the appearance of a subway vessel beneath the normal arch.
 Also be seen with MRI , in coronal or off-axis sagittal (candy cane)
sections. .
 In atresia or interruption of the superior arch, there is the appearance
of a truly common brachiocephalic trunk in which all four arch
vessels, including the left subclavian artery, arise from a single vessel
.
 At surgery for repair of coarctation of the aorta (distal to the fifth
arch), an atretic strand connecting the left subclavian artery to the
descending aorta may be seen.
 There appears to be no other plausible explanation for such a
branching pattern.
 Without additional coarctation of the existing aorta, these two arch
anomalies alone have no physiologic significance.
Interrupted Aortic Arch
 Defined as a complete separation of ascending and descending aorta.
 Celoria and Patton classification
Type A - interruption distal to the left (SCA)subclavian artery
Type B- between carotid and Lt SCA
Type C - between carotid arteries.
A B
C
Subcategores
 Interruption distal to that SCA
Without retroesophageal or isolated SCA
With retroesophageal SCA
With isolated SCA
 Interruption between second carotid and ipsilateral SCA
Without retroesophageal or isolated SCA
With retroesophageal SCA (i.e., both carotid arteries proximal,
both subclavians distal)
With isolated SCA
 Interruption between carotid arteries
Without retroesophageal or isolated SCA
With retroesophageal SCA
With isolated SCA
 Type A interruptions
-Occur with aorticopulmonary septal defect and intact ventricular
septum
-Seen in patients with transposition of the great arteries and
interrupted aortic arch .
 Type B interruptions
-More common than type A
-Usually have a conotruncal anomaly with normally aligned great
arteries in which there is a large malalignment-type VSD associated
with posterior displacement of the infundibular septum and subaortic
obstruction.
-Pts with DiGeorge syndrome have type B interuption.
 Type C interruption
-Quite rare.
In a large series of cases with DiGeorge syndrome
- 43% were found to have type B interruption, and
68% of interrupted arch patients had DiGeorge
syndrome.
This contrasts with truncus arteriosus communis in
which comparable figures were 34% and 33%,
respectively.
 Again it shows the predisposition to 4th arch
abnormality in 22q11 patients.
 Diagnosis and Management
 Presentation similar to pts with other ductal-dependent left heart
obstructive lesions, with acute cardiovascular collapse or heart failure
after spontaneous closure of the ductus arteriosus in the first days of
life.
 Initial management - fluid resuscitation, induction and maintenance of
ductal patency with PGE1, and establishment of stable
hemodynamics, with inotropic support .
 Physical findings of pulse discrepancy, depending on branching
pattern, are helpful.
 Absence of all limb pulses suggests type B interruption with
anomalous subclavian artery, i.e., both carotid arteries proximal, both
subclavians distal to the interruption.
 2D- echo is the most important tool for diagnostic imaging of
interrupted arch.
 The diagnosis should be suspected from the marked discrepancy in
size between ascending aorta and main pulmonary artery with
subcostal frontal imaging, in the presence of the typical malalignment
type VSD with posterior deviation of the infundibular (conal) septum,
best visualized in the parasternal long-axis view.
 Imaging of the arch from suprasternal or high parasternal for
determination of the branching pattern and patency of the arch
 Angiography is used to confirm the diagnosis of interrupted aortic
arch.
 Interruption can be diagnosed consistently by angiography when both
carotid arteries arise proximal to, and both subclavian arteries distal
to, the interruption.
 The wide separation of carotid arteries from descending aorta
unequivocally demonstrates interruption.
 3D reconstruction from MRI can demonstrate the branching pattern
and the separation between proximal and distal aorta .
Anomalous Origin of the LPA from RPA
( pulmonary artery sling )
 Origin of the left pulmonary artery from the right pulmonary artery
known as pulmonary artery sling , is a
 Rare anomaly in which the lower trachea is partially surrounded by
vascular structures
 The left pulmonary artery arising as a very proximal branch of the
right loops around the trachea.
 It is the only situation in which a major vascular structure passes
between the trachea and esophagus.
 It usually appears as an isolated abnormality but can be associated
with other congenital cardiac defects, including tetralogy of Fallot.
 Diagnosis and Management
 These patients typically present with severe respiratory distress and
stridor
 Barium swallow when classic is diagnostic if one can rule out
mediastinal tumor.
 Echo, angiocardiography, MRI, or CT is usually necessary to ensure
the accuracy of the diagnosis.
 Symptomatic patients should be evaluated by bronchoscopy at the
time of surgical repair because of the frequent association of complete
cartilaginous rings.
 The usual surgical approach is division of the left pulmonary artery
from the right and reanastomosis in front of the trachea.
Bovine Aortic Arch Variant in
Humans
 The bovine aortic arch in humans resemble the aortic arch branching
pattern found in the family of ruminant animals, including cattle and
buffalo.
 But bovine aortic arch configuration ascribed to the most common
human aortic arch variants have no resemblance to the aortic arch
branching pattern found in cattle.
 This is the human aortic arch branching pattern which has a common
origin for the innominate and left common carotid arteries.
 This pattern has erroneously been referred to as a “bovine arch.”
 The left common carotid artery has a common origin with the
innominate artery, rather than arising directly from the aortic arch as a
separate branch.
 A similar but less common variant occurs when the left common
carotid artery originates directly from the innominate artery rather
than as a common trunk .
 Both variants of left common carotid artery origin are called
“bovine-type arch,” .
• Thank u

Más contenido relacionado

La actualidad más candente

Aortic arch anomalies
Aortic arch anomaliesAortic arch anomalies
Aortic arch anomaliesSanket Nale
 
CORONARY ANGIOGRAPHY.pptx
CORONARY ANGIOGRAPHY.pptxCORONARY ANGIOGRAPHY.pptx
CORONARY ANGIOGRAPHY.pptxRohitWalse2
 
Valvular heart diseases imaging
Valvular heart diseases imagingValvular heart diseases imaging
Valvular heart diseases imagingDev Lakhera
 
Double outlet right ventricle
Double outlet right ventricleDouble outlet right ventricle
Double outlet right ventricleHimanshu Rana
 
Pulmonary venous hypertension stages & skiagraphic changes
Pulmonary venous hypertension  stages & skiagraphic changesPulmonary venous hypertension  stages & skiagraphic changes
Pulmonary venous hypertension stages & skiagraphic changesGOVT MEDICAL COLLEGE TRIVANDRUM
 
tetrology of fallot (TOF) with pulmonary atresia
tetrology of fallot (TOF) with pulmonary atresiatetrology of fallot (TOF) with pulmonary atresia
tetrology of fallot (TOF) with pulmonary atresiaMalleswara rao Dangeti
 
Fetal Echocardiography
Fetal EchocardiographyFetal Echocardiography
Fetal Echocardiographymadhusiva03
 
CAG interpretation Dr Shiva CTVS JIPMER
CAG interpretation   Dr Shiva CTVS JIPMERCAG interpretation   Dr Shiva CTVS JIPMER
CAG interpretation Dr Shiva CTVS JIPMERShivashankar Sadasivam
 
Ecg in congenital heart disease
Ecg in congenital heart diseaseEcg in congenital heart disease
Ecg in congenital heart diseaseRamachandra Barik
 
Sequential segmental analysis of heart
Sequential segmental analysis of heartSequential segmental analysis of heart
Sequential segmental analysis of heartKunwar Saurabh
 
Coronary cameral fistula
Coronary cameral fistula Coronary cameral fistula
Coronary cameral fistula raghdaeve
 
Peripheral arterial doppler
Peripheral  arterial dopplerPeripheral  arterial doppler
Peripheral arterial dopplerAnish Choudhary
 
Assessment of myocardial viability
Assessment of myocardial viabilityAssessment of myocardial viability
Assessment of myocardial viabilitySwapnil Garde
 
Aortic arch anomalies
Aortic arch anomaliesAortic arch anomalies
Aortic arch anomaliesSumit Shanker
 
Coarctation of aorta
Coarctation of aorta  Coarctation of aorta
Coarctation of aorta Vikas Kumar
 
Tte and tee assessment for asd closure 2
Tte and tee assessment for asd closure 2Tte and tee assessment for asd closure 2
Tte and tee assessment for asd closure 2Rahul Chalwade
 

La actualidad más candente (20)

Aortic arch anomalies
Aortic arch anomaliesAortic arch anomalies
Aortic arch anomalies
 
CORONARY ANGIOGRAPHY.pptx
CORONARY ANGIOGRAPHY.pptxCORONARY ANGIOGRAPHY.pptx
CORONARY ANGIOGRAPHY.pptx
 
Valvular heart diseases imaging
Valvular heart diseases imagingValvular heart diseases imaging
Valvular heart diseases imaging
 
SEGMENTAL ANALYSIS OF CONGENITAL HEART DISEASE
SEGMENTAL ANALYSIS OF CONGENITAL HEART DISEASE SEGMENTAL ANALYSIS OF CONGENITAL HEART DISEASE
SEGMENTAL ANALYSIS OF CONGENITAL HEART DISEASE
 
Conotruncal anamolies
Conotruncal anamoliesConotruncal anamolies
Conotruncal anamolies
 
L-TGA or CCTGA
L-TGA or CCTGA L-TGA or CCTGA
L-TGA or CCTGA
 
Double outlet right ventricle
Double outlet right ventricleDouble outlet right ventricle
Double outlet right ventricle
 
Pulmonary venous hypertension stages & skiagraphic changes
Pulmonary venous hypertension  stages & skiagraphic changesPulmonary venous hypertension  stages & skiagraphic changes
Pulmonary venous hypertension stages & skiagraphic changes
 
Cardiac venous system
Cardiac venous systemCardiac venous system
Cardiac venous system
 
tetrology of fallot (TOF) with pulmonary atresia
tetrology of fallot (TOF) with pulmonary atresiatetrology of fallot (TOF) with pulmonary atresia
tetrology of fallot (TOF) with pulmonary atresia
 
Fetal Echocardiography
Fetal EchocardiographyFetal Echocardiography
Fetal Echocardiography
 
CAG interpretation Dr Shiva CTVS JIPMER
CAG interpretation   Dr Shiva CTVS JIPMERCAG interpretation   Dr Shiva CTVS JIPMER
CAG interpretation Dr Shiva CTVS JIPMER
 
Ecg in congenital heart disease
Ecg in congenital heart diseaseEcg in congenital heart disease
Ecg in congenital heart disease
 
Sequential segmental analysis of heart
Sequential segmental analysis of heartSequential segmental analysis of heart
Sequential segmental analysis of heart
 
Coronary cameral fistula
Coronary cameral fistula Coronary cameral fistula
Coronary cameral fistula
 
Peripheral arterial doppler
Peripheral  arterial dopplerPeripheral  arterial doppler
Peripheral arterial doppler
 
Assessment of myocardial viability
Assessment of myocardial viabilityAssessment of myocardial viability
Assessment of myocardial viability
 
Aortic arch anomalies
Aortic arch anomaliesAortic arch anomalies
Aortic arch anomalies
 
Coarctation of aorta
Coarctation of aorta  Coarctation of aorta
Coarctation of aorta
 
Tte and tee assessment for asd closure 2
Tte and tee assessment for asd closure 2Tte and tee assessment for asd closure 2
Tte and tee assessment for asd closure 2
 

Similar a aortic arch anamolies

AORTIC ARCH ANOMALIES 2.pptx
AORTIC ARCH ANOMALIES 2.pptxAORTIC ARCH ANOMALIES 2.pptx
AORTIC ARCH ANOMALIES 2.pptxVishnuDutt40
 
VASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptx
VASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptxVASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptx
VASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptxJaydeep Malakar
 
Congenital aortic diseases by MSCT
Congenital aortic diseases by MSCTCongenital aortic diseases by MSCT
Congenital aortic diseases by MSCTMohamed Gibreel
 
Anatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system inAnatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system inRamachandra Barik
 
An unusual origin of brachiocephalic and left common carotid arteries 2018
An unusual origin of brachiocephalic and left common carotid arteries 2018An unusual origin of brachiocephalic and left common carotid arteries 2018
An unusual origin of brachiocephalic and left common carotid arteries 2018Dr.Srikanth pawar
 
Pediatric Cardiology (1).pptx
Pediatric Cardiology (1).pptxPediatric Cardiology (1).pptx
Pediatric Cardiology (1).pptxelgieaulia
 
Anatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system inAnatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system inGopi Krishna Rayidi
 
Congenital heart diseases2020
Congenital heart diseases2020Congenital heart diseases2020
Congenital heart diseases2020RiyadhWaheed
 
Vascular fetal anomaly -aortic arch anomalies
Vascular fetal anomaly -aortic arch anomaliesVascular fetal anomaly -aortic arch anomalies
Vascular fetal anomaly -aortic arch anomaliesMarius Bogdan Muresan
 
Vascular anomalies chest
Vascular anomalies chestVascular anomalies chest
Vascular anomalies chestfenderhm
 
Vascular development
Vascular developmentVascular development
Vascular developmentRezaul hayat
 
Anomalies of fetal cardiac system
Anomalies of fetal cardiac systemAnomalies of fetal cardiac system
Anomalies of fetal cardiac systemNISHANT RAJ
 
Aortic Arches
Aortic ArchesAortic Arches
Aortic ArchesDRHAFIZ07
 
CT in congenital heart diseases
CT in congenital heart diseasesCT in congenital heart diseases
CT in congenital heart diseasesMohamed Gibreel
 
coronary angiography, LV angiogram and coronary anomalies
coronary angiography, LV angiogram and coronary anomaliescoronary angiography, LV angiogram and coronary anomalies
coronary angiography, LV angiogram and coronary anomaliesSalman Ahmed
 

Similar a aortic arch anamolies (20)

AORTIC ARCH ANOMALIES 2.pptx
AORTIC ARCH ANOMALIES 2.pptxAORTIC ARCH ANOMALIES 2.pptx
AORTIC ARCH ANOMALIES 2.pptx
 
VASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptx
VASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptxVASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptx
VASCULAR RINGS AND SLINGS TYPES HAEMODYNAMICS PRESENTATION AND DIAGNOSIS.pptx
 
Aortic arch anomalies
Aortic arch anomaliesAortic arch anomalies
Aortic arch anomalies
 
Congenital aortic diseases by MSCT
Congenital aortic diseases by MSCTCongenital aortic diseases by MSCT
Congenital aortic diseases by MSCT
 
Anatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system inAnatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system in
 
Echocardiography of CHD in Adults
Echocardiography of CHD in AdultsEchocardiography of CHD in Adults
Echocardiography of CHD in Adults
 
Vascular ring & Sling
Vascular ring & SlingVascular ring & Sling
Vascular ring & Sling
 
An unusual origin of brachiocephalic and left common carotid arteries 2018
An unusual origin of brachiocephalic and left common carotid arteries 2018An unusual origin of brachiocephalic and left common carotid arteries 2018
An unusual origin of brachiocephalic and left common carotid arteries 2018
 
Pediatric Cardiology (1).pptx
Pediatric Cardiology (1).pptxPediatric Cardiology (1).pptx
Pediatric Cardiology (1).pptx
 
Anatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system inAnatomy of cardiac structures & conducting system in
Anatomy of cardiac structures & conducting system in
 
Congenital heart diseases2020
Congenital heart diseases2020Congenital heart diseases2020
Congenital heart diseases2020
 
Vascular fetal anomaly -aortic arch anomalies
Vascular fetal anomaly -aortic arch anomaliesVascular fetal anomaly -aortic arch anomalies
Vascular fetal anomaly -aortic arch anomalies
 
rad ana of chest.pdf
rad ana of chest.pdfrad ana of chest.pdf
rad ana of chest.pdf
 
Vascular anomalies chest
Vascular anomalies chestVascular anomalies chest
Vascular anomalies chest
 
Vascular development
Vascular developmentVascular development
Vascular development
 
Anomalies of fetal cardiac system
Anomalies of fetal cardiac systemAnomalies of fetal cardiac system
Anomalies of fetal cardiac system
 
Aortic Arches
Aortic ArchesAortic Arches
Aortic Arches
 
CT in congenital heart diseases
CT in congenital heart diseasesCT in congenital heart diseases
CT in congenital heart diseases
 
coronary angiography, LV angiogram and coronary anomalies
coronary angiography, LV angiogram and coronary anomaliescoronary angiography, LV angiogram and coronary anomalies
coronary angiography, LV angiogram and coronary anomalies
 
Vm presentation
Vm presentationVm presentation
Vm presentation
 

Más de Malleswara rao Dangeti

Approach to coronary bifurcation lesions
Approach to coronary bifurcation lesionsApproach to coronary bifurcation lesions
Approach to coronary bifurcation lesionsMalleswara rao Dangeti
 
supraventricular tachycardia (SVT) with aberrancy
supraventricular tachycardia (SVT) with aberrancysupraventricular tachycardia (SVT) with aberrancy
supraventricular tachycardia (SVT) with aberrancyMalleswara rao Dangeti
 
LEADLESS PACEMAKER AND SUBCUTANEOUS ICD
LEADLESS PACEMAKER AND SUBCUTANEOUS ICDLEADLESS PACEMAKER AND SUBCUTANEOUS ICD
LEADLESS PACEMAKER AND SUBCUTANEOUS ICDMalleswara rao Dangeti
 
Right ventricle (RV) anatomy and functions
Right ventricle (RV) anatomy and functionsRight ventricle (RV) anatomy and functions
Right ventricle (RV) anatomy and functionsMalleswara rao Dangeti
 
QRS axis change during ventricualr tachycardia (VT)
QRS axis   change during ventricualr tachycardia (VT)QRS axis   change during ventricualr tachycardia (VT)
QRS axis change during ventricualr tachycardia (VT)Malleswara rao Dangeti
 
Pliability assessment,pre procedure evaluation-tricks in difficult pbmv
Pliability assessment,pre procedure evaluation-tricks in difficult pbmvPliability assessment,pre procedure evaluation-tricks in difficult pbmv
Pliability assessment,pre procedure evaluation-tricks in difficult pbmvMalleswara rao Dangeti
 
Management of VENTRICULAR TACHYCARDIA (VT)
Management of VENTRICULAR TACHYCARDIA (VT)Management of VENTRICULAR TACHYCARDIA (VT)
Management of VENTRICULAR TACHYCARDIA (VT)Malleswara rao Dangeti
 

Más de Malleswara rao Dangeti (20)

Genetics in cardiovascular system
Genetics in cardiovascular systemGenetics in cardiovascular system
Genetics in cardiovascular system
 
TEE VIEWS
TEE VIEWSTEE VIEWS
TEE VIEWS
 
TEE VIEWS
TEE VIEWSTEE VIEWS
TEE VIEWS
 
acute rheumatic fever
acute rheumatic feveracute rheumatic fever
acute rheumatic fever
 
fundamentals of pacemaker
fundamentals of pacemaker  fundamentals of pacemaker
fundamentals of pacemaker
 
Approach to coronary bifurcation lesions
Approach to coronary bifurcation lesionsApproach to coronary bifurcation lesions
Approach to coronary bifurcation lesions
 
Treadmill test (TMT)
Treadmill test (TMT)Treadmill test (TMT)
Treadmill test (TMT)
 
Trouble shoooting ICD AND CRT
Trouble shoooting ICD AND CRTTrouble shoooting ICD AND CRT
Trouble shoooting ICD AND CRT
 
supraventricular tachycardia (SVT) with aberrancy
supraventricular tachycardia (SVT) with aberrancysupraventricular tachycardia (SVT) with aberrancy
supraventricular tachycardia (SVT) with aberrancy
 
LEADLESS PACEMAKER AND SUBCUTANEOUS ICD
LEADLESS PACEMAKER AND SUBCUTANEOUS ICDLEADLESS PACEMAKER AND SUBCUTANEOUS ICD
LEADLESS PACEMAKER AND SUBCUTANEOUS ICD
 
SINOATRIAL (SA) node
SINOATRIAL (SA) node SINOATRIAL (SA) node
SINOATRIAL (SA) node
 
relative wall thickness
relative wall thicknessrelative wall thickness
relative wall thickness
 
Right ventricle (RV) anatomy and functions
Right ventricle (RV) anatomy and functionsRight ventricle (RV) anatomy and functions
Right ventricle (RV) anatomy and functions
 
QRS axis change during ventricualr tachycardia (VT)
QRS axis   change during ventricualr tachycardia (VT)QRS axis   change during ventricualr tachycardia (VT)
QRS axis change during ventricualr tachycardia (VT)
 
Pliability assessment,pre procedure evaluation-tricks in difficult pbmv
Pliability assessment,pre procedure evaluation-tricks in difficult pbmvPliability assessment,pre procedure evaluation-tricks in difficult pbmv
Pliability assessment,pre procedure evaluation-tricks in difficult pbmv
 
STEPP AMI
STEPP AMISTEPP AMI
STEPP AMI
 
Normal variants of heart structures
Normal variants of heart structuresNormal variants of heart structures
Normal variants of heart structures
 
Management of VENTRICULAR TACHYCARDIA (VT)
Management of VENTRICULAR TACHYCARDIA (VT)Management of VENTRICULAR TACHYCARDIA (VT)
Management of VENTRICULAR TACHYCARDIA (VT)
 
Low flow low gradient aortic stenosis
Low flow low gradient aortic stenosisLow flow low gradient aortic stenosis
Low flow low gradient aortic stenosis
 
Hyponatremia in heart failure
Hyponatremia in heart failure Hyponatremia in heart failure
Hyponatremia in heart failure
 

Último

Hemostasis Physiology and Clinical correlations by Dr Faiza.pdf
Hemostasis Physiology and Clinical correlations by Dr Faiza.pdfHemostasis Physiology and Clinical correlations by Dr Faiza.pdf
Hemostasis Physiology and Clinical correlations by Dr Faiza.pdfMedicoseAcademics
 
POST NATAL EXERCISES AND ITS IMPACT.pptx
POST NATAL EXERCISES AND ITS IMPACT.pptxPOST NATAL EXERCISES AND ITS IMPACT.pptx
POST NATAL EXERCISES AND ITS IMPACT.pptxvirengeeta
 
call girls in green park DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️
call girls in green park  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️call girls in green park  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️
call girls in green park DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️saminamagar
 
Music Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara Rajendran
Music Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara RajendranMusic Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara Rajendran
Music Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara RajendranTara Rajendran
 
Hematology and Immunology - Leukocytes Functions
Hematology and Immunology - Leukocytes FunctionsHematology and Immunology - Leukocytes Functions
Hematology and Immunology - Leukocytes FunctionsMedicoseAcademics
 
Call Girls Viman Nagar 7001305949 All Area Service COD available Any Time
Call Girls Viman Nagar 7001305949 All Area Service COD available Any TimeCall Girls Viman Nagar 7001305949 All Area Service COD available Any Time
Call Girls Viman Nagar 7001305949 All Area Service COD available Any Timevijaych2041
 
Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...
Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...
Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...rajnisinghkjn
 
The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...
The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...
The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...DrGoharMushtaq
 
COVID-19 (NOVEL CORONA VIRUS DISEASE PANDEMIC ).pptx
COVID-19  (NOVEL CORONA  VIRUS DISEASE PANDEMIC ).pptxCOVID-19  (NOVEL CORONA  VIRUS DISEASE PANDEMIC ).pptx
COVID-19 (NOVEL CORONA VIRUS DISEASE PANDEMIC ).pptxBibekananda shah
 
Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...
Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...
Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...rajnisinghkjn
 
QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)
QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)
QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)Hasnat Tariq
 
epilepsy and status epilepticus for undergraduate.pptx
epilepsy and status epilepticus  for undergraduate.pptxepilepsy and status epilepticus  for undergraduate.pptx
epilepsy and status epilepticus for undergraduate.pptxMohamed Rizk Khodair
 
SWD (Short wave diathermy)- Physiotherapy.ppt
SWD (Short wave diathermy)- Physiotherapy.pptSWD (Short wave diathermy)- Physiotherapy.ppt
SWD (Short wave diathermy)- Physiotherapy.pptMumux Mirani
 
call girls in GTB Nagar Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...
call girls in GTB Nagar Metro  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...call girls in GTB Nagar Metro  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...
call girls in GTB Nagar Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...saminamagar
 
PERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptx
PERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptxPERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptx
PERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptxdrashraf369
 
call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...
call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...
call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...saminamagar
 
Apiculture Chapter 1. Introduction 2.ppt
Apiculture Chapter 1. Introduction 2.pptApiculture Chapter 1. Introduction 2.ppt
Apiculture Chapter 1. Introduction 2.pptkedirjemalharun
 
PNEUMOTHORAX AND ITS MANAGEMENTS.pdf
PNEUMOTHORAX   AND  ITS  MANAGEMENTS.pdfPNEUMOTHORAX   AND  ITS  MANAGEMENTS.pdf
PNEUMOTHORAX AND ITS MANAGEMENTS.pdfDolisha Warbi
 
LUNG TUMORS AND ITS CLASSIFICATIONS.pdf
LUNG TUMORS AND ITS  CLASSIFICATIONS.pdfLUNG TUMORS AND ITS  CLASSIFICATIONS.pdf
LUNG TUMORS AND ITS CLASSIFICATIONS.pdfDolisha Warbi
 
Measurement of Radiation and Dosimetric Procedure.pptx
Measurement of Radiation and Dosimetric Procedure.pptxMeasurement of Radiation and Dosimetric Procedure.pptx
Measurement of Radiation and Dosimetric Procedure.pptxDr. Dheeraj Kumar
 

Último (20)

Hemostasis Physiology and Clinical correlations by Dr Faiza.pdf
Hemostasis Physiology and Clinical correlations by Dr Faiza.pdfHemostasis Physiology and Clinical correlations by Dr Faiza.pdf
Hemostasis Physiology and Clinical correlations by Dr Faiza.pdf
 
POST NATAL EXERCISES AND ITS IMPACT.pptx
POST NATAL EXERCISES AND ITS IMPACT.pptxPOST NATAL EXERCISES AND ITS IMPACT.pptx
POST NATAL EXERCISES AND ITS IMPACT.pptx
 
call girls in green park DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️
call girls in green park  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️call girls in green park  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️
call girls in green park DELHI 🔝 >༒9540349809 🔝 genuine Escort Service 🔝✔️✔️
 
Music Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara Rajendran
Music Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara RajendranMusic Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara Rajendran
Music Therapy's Impact in Palliative Care| IAPCON2024| Dr. Tara Rajendran
 
Hematology and Immunology - Leukocytes Functions
Hematology and Immunology - Leukocytes FunctionsHematology and Immunology - Leukocytes Functions
Hematology and Immunology - Leukocytes Functions
 
Call Girls Viman Nagar 7001305949 All Area Service COD available Any Time
Call Girls Viman Nagar 7001305949 All Area Service COD available Any TimeCall Girls Viman Nagar 7001305949 All Area Service COD available Any Time
Call Girls Viman Nagar 7001305949 All Area Service COD available Any Time
 
Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...
Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...
Dwarka Sector 24 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few C...
 
The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...
The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...
The New Standard of Care__Leveraging the Benefits of SGLT2 Inhibitors Across ...
 
COVID-19 (NOVEL CORONA VIRUS DISEASE PANDEMIC ).pptx
COVID-19  (NOVEL CORONA  VIRUS DISEASE PANDEMIC ).pptxCOVID-19  (NOVEL CORONA  VIRUS DISEASE PANDEMIC ).pptx
COVID-19 (NOVEL CORONA VIRUS DISEASE PANDEMIC ).pptx
 
Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...
Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...
Dwarka Sector 2 Call Girls ( 9873940964 ) Book Hot And Sexy Girls In A Few Cl...
 
QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)
QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)
QUALITY CONTROL OF SOLID DOSAGE FORMS (TABLETS , CAPSULES & POWDERS)
 
epilepsy and status epilepticus for undergraduate.pptx
epilepsy and status epilepticus  for undergraduate.pptxepilepsy and status epilepticus  for undergraduate.pptx
epilepsy and status epilepticus for undergraduate.pptx
 
SWD (Short wave diathermy)- Physiotherapy.ppt
SWD (Short wave diathermy)- Physiotherapy.pptSWD (Short wave diathermy)- Physiotherapy.ppt
SWD (Short wave diathermy)- Physiotherapy.ppt
 
call girls in GTB Nagar Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...
call girls in GTB Nagar Metro  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...call girls in GTB Nagar Metro  DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...
call girls in GTB Nagar Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Service ...
 
PERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptx
PERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptxPERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptx
PERFECT BUT PAINFUL TKR -ROLE OF SYNOVECTOMY.pptx
 
call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...
call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...
call girls in Dwarka Sector 21 Metro DELHI 🔝 >༒9540349809 🔝 genuine Escort Se...
 
Apiculture Chapter 1. Introduction 2.ppt
Apiculture Chapter 1. Introduction 2.pptApiculture Chapter 1. Introduction 2.ppt
Apiculture Chapter 1. Introduction 2.ppt
 
PNEUMOTHORAX AND ITS MANAGEMENTS.pdf
PNEUMOTHORAX   AND  ITS  MANAGEMENTS.pdfPNEUMOTHORAX   AND  ITS  MANAGEMENTS.pdf
PNEUMOTHORAX AND ITS MANAGEMENTS.pdf
 
LUNG TUMORS AND ITS CLASSIFICATIONS.pdf
LUNG TUMORS AND ITS  CLASSIFICATIONS.pdfLUNG TUMORS AND ITS  CLASSIFICATIONS.pdf
LUNG TUMORS AND ITS CLASSIFICATIONS.pdf
 
Measurement of Radiation and Dosimetric Procedure.pptx
Measurement of Radiation and Dosimetric Procedure.pptxMeasurement of Radiation and Dosimetric Procedure.pptx
Measurement of Radiation and Dosimetric Procedure.pptx
 

aortic arch anamolies

  • 2.  Hunault in 1735,cited by Moes -wrote pathologic description of anomalous right subclavian artery.  Double aortic arch-Hunault 1735  First report of clinical syndrome of vascular compression-wolman 1939  Kommerel in 1936 –xray findings of anamolous right sca  first division of a vascular ring -Gross in 1945  first successful repair of interrupted aortic arch-Merrill et al. in 1957 .
  • 3. classifications • Stewert etal and shuford ,syber etal – Side of aortic arch – Origin of brachiocephalic vessels – Site of DA/LA • Freedom etal-vascular ring/sling/compression • sissman-Ao.arch position,course,length,size
  • 4. Anatomical Classification  following anatomic categories: 1)Abnormalities of branching, 2)Abnormalities of arch position including right aortic arch & cervical aortic arch, 3)Supernumerary arches including double aortic arch and persistent fifth aortic arch, 4)Interrupted aortic arch 5)Anomalous origin of a pulmonary artery branch from the ascending aorta or from the contralateral pulmonary artery branch.
  • 5. Embryology  The specific anomalies better understood through appreciation of their embryologic origins.  Development of the aortic arch system - best be described as- sequential appearance and persistence or regression of 6 paired vessels connecting the truncoaortic sac of the embryonic heart tube with the paired dorsal aortae, which fuse to form the definitive descending aorta.
  • 6.
  • 7. • Fate of the aortic arches:  First pair: A small part forms the maxillary artery, the rest disappears.  Second pair: A small part forms the stapedial & hyoid arteries, the rest disappears.  Third pair: forms the common, internal & external carotid arteries on each side.  Fourth pair: forms the aortic arch (AA) on the left side, and the right subclavian (RSC) artery on the right side.  Fifth pair: totally disappears.  Sixth pair: forms the right & left pulmonary arteries (PA) and the ductus arteriosus (DA).
  • 8. Left and Right Arch Definition  Left and right aortic arch- refer to which bronchus is crossed by the arch, not to which side of the midline the aortic root ascends.  Sidedness determined with Echo or angiography by the branching pattern of the brachiocephalic vessels.  General rule – 1st arch vessel contain a carotid artery. contralateral to Aortic Arch
  • 9. The 3 brachiocephalic br. of the arch are derived from: - The innominate artery -Rt br. of the truncoaortic sac - Rt common carotid artery-Rt 3rd embryonic arch - Rt subclavian -Rt 4th arch and (proximal) Rt dorsal aorta proximally and Rt 7th ISA distally; - Lt carotid artery -Lt 3rd aortic arch; - Lt subclavian artery from Lt 7th ISA.
  • 10. Diagnostic Methods  1930s, barium esophagography - primary method for diagnosing arch anomalies.  In the 1960s and 1970s, angiography became the gold standard .  In the last 10 to 15 years, MRI and CT, have supplanted angiography as the gold standard for definitive diagnosis of arch anomalies.  Both modalities have the advantages of large fields of view and simultaneous visualization of vessels and airways, and both are minimally invasive.
  • 12. Clinical Classification  In addition to the anatomic categorization , arch anomalies divided according to clinical features as follows: -Vascular rings; -Non ring vascular compression of the trachea, bronchi, or esophagus; - Noncompressive arch malformations; -Ductal-dependent arch anomalies including interrupted aortic arches - Isolated subclavian, carotid, or innominate arteries. - Genetic syndromes and associated abnormalities.
  • 13. Vascular Rings  In this anomaly trachea and esophagus are completely surrounded by vascular structures.  The vascular structures need not be patent, e.g., a ligamentum arteriosum or atretic segment of aortic arch may complete a ring.  clinical presentation - stridor, pneumonia, bronchitis, or cough .  Infants may - posture of hyperextension of the neck.  Less commonly, pts exhibit reflex apnea associated with eating..  Less commonly in toddlers or older children- swallowing difficulty or choking .
  • 14.  When all elements of the ring are patent, visualization, especially by tomographic imaging, is straightforward.  In cases where the ring is completed by an atretic segment of aorta or ligamentum arteriosum, those segments cannot be visualized with current imaging technologies.  But these rings are recognizable by the presence of one of three opposite the side of the aortic arch: diverticulum, dimple, or descending aorta .
  • 15. Normal Left Aortic Arch and variants  normal left aortic arch crosses the left mainstem bronchus at T5 and descends left of the midline to the diaphragm and beyond in cases of visceral situs solitus.  normal branching pattern has the right innominate artery first.  branches into the Rt CCA and Rt subclavian arteries  Lt carotid artery second, and the Lt subclavian artery third.  Ductus arteriosus or the ligamentum arteriosum joins the aorta distal to Lt subclavian artery .
  • 16.  2 frequent variants of the Lt aortic arch.  -1)Common brachiocephalic trunk, in which the right innominate and left carotid arteries arise from a single origin. Present in10% of otherwise normal left arches No consequence, Some have suggested that innominate artery compression of the trachea is more frequent when common brachiocephalic trunk is present. -
  • 17. 2)Separate origin of the Lt vertebral artery from the aortic arch proximal to the takeoff of the lt SCA rather than from the SCA . • Seen in 10% of normal left arches ,No functional significance • • should not be confused with anomalous Rt SCA in which there are also four brachiocephalic vessels . • Distinguishing feature 3-D MRI of normal variant with separate origin of left vertebral artery (L Vert) from the aortic arch
  • 18. Left Aortic Arch with Retroesophageal Rt SCA  first described by Hunauld in 1735.  Also called anomalous or aberrant right subclavian artery  Bayford coined the term dysphagia lusoria•(from the Latin, lusus naturae, trick of nature).  The branching pattern 1st branch - Rt CCA 2nd - Lt CCA 3rd - Lt SCA 4th - retroesophageal Rt SCA arising from the posteromedial aspect of the distal aortic arch
  • 19.
  • 20.  Most common arch anomaly,  Seen in 0.5% of the general population.  The incidence in Down syndrome patients with congenital heart disease is very high at 38% .  Mostly asymptomatic, with the diagnosis made while imaging for another condition or at autopsy.
  • 21. assoc • TOF and left aortic arch- • COA- – may arise distal to coarct site. If so: – BP in RUL and LL does not reflect coarct. Gradient – Rib notching seen only on left side
  • 22.  Diagnosis and Management  Since there is no innominate artery, 1st & 2nd branches, (Rt&Lt CA) similar in size as are the last 2 branches( Lt &Rt SCA)  Barium esophagography - Fixed filling defect usually slanting upward to the right  Angiography -The diagnosis may sometimes be missed in the AP projection since the right subclavian may be superimposed on the right carotid artery in the usual position. - Careful single-frame analysis will demonstrate the earlier filling of the right carotid on an aortic root injection or the earlier filling of the right subclavian on a descending aortic injection.
  • 24. Echocardiography - -Branching pattern , a nonbifurcating first branch that ascends toward the right, followed by two successive left-sided vessels (left carotid and left subclavian arteries) followed by a fourth branch that heads toward the right but may disappear behind the trachea.  MRI - The retroesophageal course of the subclavian artery is shown on transverse (axial) cuts.
  • 25. • If symptomatic- – Division of anamolous RSCA – Dissection of retroesophageal component if any – Reanastomosis of vessel • Establishing flow in RSCA- important. • Approach in pt with vascular ring- – right thoracotomy
  • 26. Left Aortic Arch with Retroesophageal Diverticulum of Kommerell  Very rare arch anomaly  1st vascular ring to be diagnosed in life with barium esophagography by Kommerell  branching pattern identical to that of the more common left arch with retroesophageal right subclavian artery  The difference is in the caliber of the proximal subclavian artery .  significance - is that the abrupt change of vessel size always indicates the presence of a ligamentum arteriosum, which completes a vascular ring.
  • 27. Left Aortic Arch with Right Descending Aorta and Right Ductus (or Ligamentum)  Rare arch anomaly, also known as circumflex aortic arch, with a branching pattern similar to that of left arch with retroesophageal right subclavian artery.  The arch itself is retroesophageal; hence the right subclavian artery, although it may arise as the last arch vessel, is not retro-esophageal .  The descending aorta is connected by a ductus or ligamentum to the right pulmonary artery, forming a vascular ring.
  • 28.
  • 29. Left Aortic Arch with Isolated SCA  Rare anomaly, subclavian artery arises only from the ductus arteriosus.  If ductus is patent, the subclavian and vertebral arteries are supplied from the pulmonary artery.  When the ductus closes, the subclavian is supplied by retrograde flow from the vertebral artery via the circle of Willis.  Embryology  This occurs with dissolution of the right fourth arch and right dorsal aorta but persistence of the right sixth arch.
  • 30.
  • 31.  Diagnosis and Management  in the absence of other anomalies, it may go unrecognized or may cause vertebrobasilar insufficiency with so-called congenital subclavian steal.  With phase-encoded velocity mapping, retrograde flow in the vertebral artery can be detected on MRI.  Symptomatic patients are treated by implantation of the subclavian artery into the aorta.
  • 32. Left Aortic Arch with Cervical Origin of the Right Subclavian Artery  Found in pts with TOF, with or without pulmonary atresia,  Seen only in patients with 22q11 deletion .  marker for CATCH 22.  Normally the right innominate artery bifurcates into a Rt CCA and Rt SCA near its origin from the aorta .  In this Innominate trifurcates in the neck, giving rise to external and internal carotids and the SCA, which then travels caudally back to the thorax.
  • 33.  Embryology Rt subclavian artery originates from the third arch, which is more cephalad than the fourth, gives origin to the subclavian artery in the neck rather than in the thorax.
  • 34. Right Aortic Arch  A single aortic arch that crosses over the right main stem bronchus, passing to the right of the trachea.  There are four major types of right arch: (a) with mirror image branching, (b) with retroesophageal left subclavian artery, (c) with retro-esophageal diverticulum, and (d) with left descending aorta. There are also several infrequently occurring variations.  Incidence - InTOF 13% to 34% . Of these-93% mirror image br -TA -36%-( generally higher than in TOF) DORV-20% -TGA 3%(assoc with VSD and PS 16%)
  • 35. Right Aortic Arch with Mirror-Image Branching  1st branch is Lt innominate artery, divides into Lt carotid and Lt SCA  2nd Rt carotid, 3rd a Rt subclavian .  left-right mirror of a normal left aortic arch.  But ..  ductus arteriosus (or ligamentum arteriosum) is usually the left-sided one, arising from the base of the innominate artery rather than from the aortic arch.  Therefore ligamentum does not form a vascular ring.  Almost always associated with congenital intracardiac disease.
  • 36.
  • 37.  Diagnosis and Management  usually produces no retro-esophageal compression or vascular ring,  no symptoms produced by the arch itself.  Diagnosis - usually made during imaging of the assoc congenital intracardiac disease.  Diagnosed by distinctive branching pattern in echo and angiography, and appearance of a right-sided indentation of trachea and esophagus on plain radiograph and barium esophagography.
  • 38.  No treatment of right aortic arch is required  It may be helpful for surgeons to know the sidedness of the aortic arch in certain circumstances.  For the classical B –T shunt and modified form are best carried out using the side with an innominate artery.
  • 39. Right Aortic Arch with Retroesophageal Diverticulum of Kommerell  Second most common vascular ring after double aortic arch.  Branching 1st branch -Lt CCA 2nd Rt CCA 3rd Rt SCA 4th - a retro-esophageal vessel from which the Lt SCA arises and the left ductus arteriosus or ligamentum arteriosum connects.  This combination of vessels produces a vascular ring.
  • 40.
  • 41.  Diagnosis and Management  The presenting symptoms are usually that of a vascular ring.  Appearance of a right aortic arch on a plain CXR . .  . Echo -Lt carotid artery arising alone as the first arch vessel, -Diverticulum followed to the point at which the caliber changes to that of the smaller subclavian artery.  Angiography- characteristic branching pattern - abrupt change in caliber from diverticulum to subclavian artery.  MRI - ideal for making this diagnosis - noninvasive and have the ability to display both vascular and airway structures.
  • 42.  Most people are asymptomatic.  Treatment is surgical division of the ductus or ligamentum in those patients who are symptomatic.  In those patients undergoing surgery for another lesion, even an asymptomatic ligamentum should be divided.
  • 43. Right Aortic Arch with Retroesophageal Left Subclavian Artery  Arch passing to the right of the trachea  Sequence of brachiocephalic arteries: - Left carotid, - Right carotid, - Right subclavian, - and retroesophageal left subclavian .  This differs from the previous arch in that the proximal left subclavian artery is not significantly larger in caliber than its more distal portion (i.e., no aortic diverticulum).  Therefore, there is no left-sided ductus arteriosus or ligamentum arteriosum and thus no vascular ring.  Many of these patients have associated conotruncal anomalies.
  • 44.  Diagnosis and Management  suspected from barium EsoG -a relatively small posterior indentation on the esophagus passing upward to the left.  No vascular ring, the trachea is unaffected except for the slight leftward deviation .  Echo- identify the first branch of the aorta as a left carotid artery  Both MRI and angiography can demonstrate the size of the left subclavian artery, which distinguishes this lesion from right aortic arch with retroesophageal diverticulum.  Since there is no vascular ring, there is usually no need for treatment other than that of associated anomalies.
  • 45. Right Aortic Arch with Left Descending Aorta and Left Ductus Arteriosus or Ligamentum Arteriosum  Also known as right aortic arch with retroesophageal segment or circumflex right aortic arch  Presentation similar to right arch with retro-esophageal diverticulum  It is the aortic arch that is retroesophageal, not the subclavian artery or an aortic diverticulum.
  • 46. Diagnosis and Management The findings on CXR and barium esophagography may be similar to those in right arch with retroesophageal diverticulum.  Differences include a downward to the left instead of upward to the left orientation of the esophageal indentation .
  • 47.  Order of brachiocephalic artery branching.  In the case of right aortic arch with left descending aorta, the first vessel contains the left carotid artery.  MRI can avoid some of the pitfalls seen with projection images and can delineate the entire aorta, its relationship to the trachea .  Division of the vascular ring when patients are symptomatic.
  • 48. Right Aortic Arch with Retroesophageal Innominate Artery  Rare abnormality of the aortic arch system.  Contrary to the general rule that the first arch vessel contains a carotid artery contralateral to the aortic arch, in these cases the sequence of brachiocephalic vessels is right carotid, right subclavian, retroesophageal left innominate artery .  The ductus arteriosus or ligamentum arteriosum completes a vascular ring as it connects the left pulmonary artery with the base of the so- called innominate artery.
  • 49.  Diagnosis and Management  Tracheal compression seems to be the rule.  The important anatomic clues to the diagnosis by any imaging modality are the presence of a single carotid artery arising from the proximal aorta.  The other anomalies with that finding are also rare: Interrupted aortic arch with interruption between the two carotid arteries and isolated left carotid or innominate artery.
  • 50. Cervical Aortic Arch  Rare anomaly ,  Apex above the clavicle (as high as the C2 ).  Seperate origin of carotid artery contralateral to arch with seperate origin if ICA,ECA,SCA on arch side  2 main subcategories - Those with anomalous subclavian artery and vascular ring, with either descending aorta c/l to the arch or retroesophageal diverticulum -And those with a virtual normal branching pattern.  The first and larger group usually has a right aortic arch. .  Separate origin of the vertebral artery from the arch can be seen in each of the groups.  The second group typically has a left aortic arch. .  Stenosis or atresia of the origin of the left subclavian artery is sometimes seen in either group .
  • 51.
  • 52.  Diagnosis and Management  Presents as pulsatile masses in the supraclavicular fossa or in the neck.  In infants, prior to the appearance of mass, presenting signs may be those of a vascular ring like , stridor, dyspnea, or repeated LRTI.  In adult, the most likely symptom from a vascular ring is dysphagia.  In patients with stenosis or atresia of the left subclavian artery and origin of the ipsilateral vertebral artery distal to the obstruction, a subclavian steal may exist with CNS symptomatology.  In the presence of a pulsatile neck mass, brief compression of the mass results in loss of femoral pulses .
  • 53.  CXR -cervical arch may be suspected by the presence of a widened upper mediastinum and the absence of the aortic knob.  Evidence of anterior deviation of the trachea is in favor of the diagnosis.  Treatment is necessary if the cervical arch is complicated by arch hypoplasia, symptomatic vascular ring, or rarely, aneurysm of the cervical arch itself .
  • 54.  Persistance of both emb.aortic arches with separate origin of CA and SCA  therefore-NO innominate artery  DA-almost always left sided  A ductus arteriosus or ligamentum may be present-not an essential element but length may affect-degree of compression  both arches-usually patent although one is larger Double Aortic Arch
  • 55. When desc. Aorta is to left of spine- Right arch –larger –more posterior-75% cases(MC) The right arch is the more superiorly located. When desc.aorta is right of spine-left arch –more posterior-larger-75-85% cases Rule-desc aorta is contralateral to side of dominant arch All double aortic arches technically form complete vascular rings around the trachea and esophagus. Usually occurs without assoc. CHD.but assoc-22% cases-TOF ,TGA
  • 56. • Although hypoplasia is common segmental atresia uncommon usually left. • Shuford and sybers classification
  • 57.
  • 58.  Embryology  Persistance of both paired dorsal aortic arches –failure of regression of right 8th somatic segment of right dorsal aorta  Right DA regresses in majority  One of the arch may be atretic- may occur at any segment  Complete vascular ring  Peristance of DA on either side not needed to complete vasc.ring like other forms .  Double arch with atretic left arch is more commonly associated with 22q11 deletions syndromes than double arch with both widely patent.
  • 59.
  • 60.
  • 61.
  • 62.  Diagnosis and Management  MC clinically recognised form of vascular ring  Severely sympto.-infancy-stridor,dyspnea,cough,recurRTI.  Feed poorly,  Prefer opisthotonus  Life threatening episodes of reflex apnea with cyanosis may.  Routine chest xray often suggests.  Hyperinflation of either/both lungs  Barium esophagography-b/l indentations of eso in AP proj  Large oblique defect(retroeso arch)  But often not possible to diff from right arch with ana.Left SCA  Angiography of asc aorta.
  • 63. The diagnosis of double arch with both arches patent can sometimes be made convincingly from the plain CXR. The tracheal air column is indented by the more superior, right-sided arch and the more inferior left arch. In the lateral view, the right arch can be seen to indent the trachea posteriorly.
  • 64.  Confirmation by echo, angiography, or MRI is important to identify the hypoplastic segment to divide it. .  Echo-Suprasternal views-coronal plane-b/l echolucencies of double arch .  MRI-side of dominant arch and patency of minor arch- spatial relationships of vessels, trachea, and esophagus for surgical planning .  Surgical division of the vascular ring in any patient who is symptomatic with airway or esophageal compression or in a patient undergoing surgery for intracardiac disease.
  • 65. Persistent Fifth Aortic Arch  First reported in man by Van Praagh in 1969 as a double-lumen aortic arch in which both arches appear on the same side of the trachea.  In double aortic arch each arch is on the opposite side.  Subcategorization : - Double-lumen aortic arch with both lumina patent -Atresia or interruption of the superior arch with patent inferior (persistent fifth) arch common origin of all brachiocephalic vessels from the ascending aorta .
  • 66.  Diagnosis and Management  Recognized either by angiography or at postmortem examination, with the appearance of a subway vessel beneath the normal arch.  Also be seen with MRI , in coronal or off-axis sagittal (candy cane) sections. .  In atresia or interruption of the superior arch, there is the appearance of a truly common brachiocephalic trunk in which all four arch vessels, including the left subclavian artery, arise from a single vessel .
  • 67.  At surgery for repair of coarctation of the aorta (distal to the fifth arch), an atretic strand connecting the left subclavian artery to the descending aorta may be seen.  There appears to be no other plausible explanation for such a branching pattern.  Without additional coarctation of the existing aorta, these two arch anomalies alone have no physiologic significance.
  • 68. Interrupted Aortic Arch  Defined as a complete separation of ascending and descending aorta.  Celoria and Patton classification Type A - interruption distal to the left (SCA)subclavian artery Type B- between carotid and Lt SCA Type C - between carotid arteries. A B C
  • 69. Subcategores  Interruption distal to that SCA Without retroesophageal or isolated SCA With retroesophageal SCA With isolated SCA  Interruption between second carotid and ipsilateral SCA Without retroesophageal or isolated SCA With retroesophageal SCA (i.e., both carotid arteries proximal, both subclavians distal) With isolated SCA  Interruption between carotid arteries Without retroesophageal or isolated SCA With retroesophageal SCA With isolated SCA
  • 70.  Type A interruptions -Occur with aorticopulmonary septal defect and intact ventricular septum -Seen in patients with transposition of the great arteries and interrupted aortic arch .  Type B interruptions -More common than type A -Usually have a conotruncal anomaly with normally aligned great arteries in which there is a large malalignment-type VSD associated with posterior displacement of the infundibular septum and subaortic obstruction. -Pts with DiGeorge syndrome have type B interuption.  Type C interruption -Quite rare.
  • 71. In a large series of cases with DiGeorge syndrome - 43% were found to have type B interruption, and 68% of interrupted arch patients had DiGeorge syndrome. This contrasts with truncus arteriosus communis in which comparable figures were 34% and 33%, respectively.  Again it shows the predisposition to 4th arch abnormality in 22q11 patients.
  • 72.  Diagnosis and Management  Presentation similar to pts with other ductal-dependent left heart obstructive lesions, with acute cardiovascular collapse or heart failure after spontaneous closure of the ductus arteriosus in the first days of life.  Initial management - fluid resuscitation, induction and maintenance of ductal patency with PGE1, and establishment of stable hemodynamics, with inotropic support .  Physical findings of pulse discrepancy, depending on branching pattern, are helpful.  Absence of all limb pulses suggests type B interruption with anomalous subclavian artery, i.e., both carotid arteries proximal, both subclavians distal to the interruption.
  • 73.  2D- echo is the most important tool for diagnostic imaging of interrupted arch.  The diagnosis should be suspected from the marked discrepancy in size between ascending aorta and main pulmonary artery with subcostal frontal imaging, in the presence of the typical malalignment type VSD with posterior deviation of the infundibular (conal) septum, best visualized in the parasternal long-axis view.  Imaging of the arch from suprasternal or high parasternal for determination of the branching pattern and patency of the arch
  • 74.  Angiography is used to confirm the diagnosis of interrupted aortic arch.  Interruption can be diagnosed consistently by angiography when both carotid arteries arise proximal to, and both subclavian arteries distal to, the interruption.  The wide separation of carotid arteries from descending aorta unequivocally demonstrates interruption.  3D reconstruction from MRI can demonstrate the branching pattern and the separation between proximal and distal aorta .
  • 75. Anomalous Origin of the LPA from RPA ( pulmonary artery sling )  Origin of the left pulmonary artery from the right pulmonary artery known as pulmonary artery sling , is a  Rare anomaly in which the lower trachea is partially surrounded by vascular structures  The left pulmonary artery arising as a very proximal branch of the right loops around the trachea.  It is the only situation in which a major vascular structure passes between the trachea and esophagus.  It usually appears as an isolated abnormality but can be associated with other congenital cardiac defects, including tetralogy of Fallot.
  • 76.
  • 77.  Diagnosis and Management  These patients typically present with severe respiratory distress and stridor  Barium swallow when classic is diagnostic if one can rule out mediastinal tumor.  Echo, angiocardiography, MRI, or CT is usually necessary to ensure the accuracy of the diagnosis.  Symptomatic patients should be evaluated by bronchoscopy at the time of surgical repair because of the frequent association of complete cartilaginous rings.  The usual surgical approach is division of the left pulmonary artery from the right and reanastomosis in front of the trachea.
  • 78. Bovine Aortic Arch Variant in Humans  The bovine aortic arch in humans resemble the aortic arch branching pattern found in the family of ruminant animals, including cattle and buffalo.  But bovine aortic arch configuration ascribed to the most common human aortic arch variants have no resemblance to the aortic arch branching pattern found in cattle.
  • 79.  This is the human aortic arch branching pattern which has a common origin for the innominate and left common carotid arteries.  This pattern has erroneously been referred to as a “bovine arch.”  The left common carotid artery has a common origin with the innominate artery, rather than arising directly from the aortic arch as a separate branch.
  • 80.  A similar but less common variant occurs when the left common carotid artery originates directly from the innominate artery rather than as a common trunk .  Both variants of left common carotid artery origin are called “bovine-type arch,” .

Notas del editor

  1. Appearance and loss of vessels as arches or portions of the brachiocephalic vasculature is sequential Edwards proposed the concept of a hypothetical double aortic arch which is, the potential contribution of nearly all embryonic arches to components of the definitive arch system. These diagrams are used extensively in the excellent monograph by Stewart, Kincaid, and Edwards (15). They are invaluable not only to demonstrate possible embryologic explanations for each arch anomaly but also to help the diagnostician determine possible and probable arch anomalies and their corresponding sequences of arch vessels.
  2. A diverticulum is a large vessel arising from the descending aorta that gives rise to a smaller-caliber vessel with a sudden taper. A dimple is a tapered, blindly ending outpouching from the aorta. Descending aorta opposite the side of the aortic arch refers to the location of the descending aorta in the upper thorax. These three occur only when connected by a ligamentum arteriosum or an atretic segment of aortic arch.
  3. : Embryonic arch diagram showing dissolution of right fourth arch and left sixth arch and persistence of right sixth arch remnant, namely, right ligamentum (R Lig (VI)).
  4. Right aortic arch with retroesophageal innominate artery. A: Left anterior oblique view of 3-D reconstruction from MRI showing LCA and LSCA arising from a single vessel, left innominate artery (Left Innom), from the D Ao. B: Diagram of embryonic arch contributions. Dissolution of left limb of truncoaortic sac (L TA Sac) with connection of left third arch to left dorsal aorta. R TA Sac, right limb of truncoaortic sac